Journal of the Hong Kong College of Cardiology

Volume 9 Number 3, July 2001

Arrhythmogenic Right Ventricular Cardiomyopathy in Chinese Patients

Wing-Hong Fung, Chi-Kin Chan, John E Sanderson

From Division of Cardiology, Department of Medicine and Therapeutics, Prince of Wales Hospital, The Chinese University of Hong Kong, Hong Kong

FUNG et al.: Arrhythmogenic Right Ventricular Cardiomyopathy in Chinese Patients. Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a familial form of cardiomyopathy predominantly affecting the right ventricle but may progress to involve the left ventricle as well. At the late stage of the disease, it is sometimes difficult to differentiate with other forms of dilated cardiomyopathy. In most affected families, the mode of inheritance of the disease is autosomal dominant. Lately, the gene accounting for the autosomal recessive form of ARVC, which was associated with palmoplantar keratosis, was identified. ARVC can present with sudden cardiac death without any preceding symptoms in the young population. Therefore, ARVC must be included in the differential diagnosis in patient surviving an episode of sudden cardiac arrest, especially in those with positive family history of sudden cardiac death. Most of the information about ARVC comes from Europe and United States. This article aims to provide a brief review of ARVC and the clinical characteristic of the disease in our local population.(J HK Coll Cardiol 2001;9:149-152)

Key words : Arrhythmogenic right ventricular cardiomyopathy

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